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alpha-N-Acetylgalactosaminidase

More information in Books or onNLM PubMed
Definition: A hexosaminidase with specificity for terminal non-reducing N-acetyl-D-galactosamine residues in N-acetyl-alpha-D-galactosaminides.      Other names endo alpha N Acetylgalactosaminidase; endo N Acetyl alpha D Galactosamidase; alpha N Acetylgalactosaminidase; alpha N Acetyl D galactosaminidase; alpha Galactosidase B; alpha D N Acetylgalactosaminyloligosaccharidase; alpha D N Acetyl Galactosaminyloligosaccharidase; N Acetyl alpha D Galactosaminidase; endo-alpha-N-Acetylgalactosaminidase; endo-N-Acetyl-alpha-D-Galactosamidase; alpha-Galactosidase B; alpha-D-N-Acetylgalactosaminyloligosaccharidase; alpha-D-N-Acetyl-Galactosaminyloligosaccharidase; N-Acetyl-alpha-D-Galactosaminidase; alpha-N-Acetyl-D-galactosaminidase
 
SubstanceCAS Registry & nameCategoriesSourceDrugs*
Lysosomal Alpha-N-Acetylgalactosaminidase Deficiency  0   *Lysosomal Storage Diseases alpha-N-Acetylgalactosaminidase/deficiency.
Kanzaki disease  0   *Lysosomal Storage Diseases alpha-N-Acetylgalactosaminidase/deficiency.
Schindler disease, type 1  0   *Lysosomal Storage Diseases *Neuroaxonal Dystrophies alpha-N-Acetylgalactosaminidase/deficiency.
gana-1 protein, C elegans  EC 3.2.1.49   *Caenorhabditis elegans Proteins *alpha-N-Acetylgalactosaminidase. BMC Cell Biol 2005;6(1):5
Naga protein, mouse  EC 3.2.1.49   *alpha-N-Acetylgalactosaminidase.
NAGA protein, human  EC 3.2.1.49   *alpha-N-Acetylgalactosaminidase.
alpha-N-acetygalactosaminidase, Acremonium  EC 3.2.1.49   *Fungal Proteins *alpha-N-Acetylgalactosaminidase. Arch Biochem Biophys 2000 Dec 15;384(2):305-10

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Sources: NLM Medical Subject Headings, NIH UMLS, Drugs@FDA, FDA AERS original data copyright United States Government. No endorsement implied. Last modified 6/6/2012

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